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Primary Sjögren’s syndrome with polymyositis, a rare amalgamation


Sjögren’s syndrome is characterized by diminished lacrimal and salivary gland secretory function. This disorder is not strictly confined to the exocrine glands and its manifestations may extend to extraglandular sites, such as the lungs, kidneys, reticuloendothelial system, and the musculoskeletal system. Although muscular manifestations are very common with Sjögren’s syndrome, true myopathy is very rare. Here, we report a case of a 45-year-old woman who presented with complaints of bilateral progressive weakness of upper and lower limbs associated with difficulty in neck holding with a history of dryness of the mouth and the eyes. The diagnosis of polymyositis associated with Sjögren’s syndrome was established on the basis of clinical picture and diagnostic tests. True polymyositis is very rare in primary Sjögren syndrome and there are scarcely any cases of primary Sjögren’s syndrome with polymyositis reported in the literature.


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Correspondence to Deepak Jain MD.

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Singh, H., Jain, D., B, K. et al. Primary Sjögren’s syndrome with polymyositis, a rare amalgamation. Egypt Rheumatol Rehabil 45, 39–41 (2018).

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  • myopathy
  • polymyositis
  • Sjögren’s
  • syndrome