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Eosinophilic granulomatosis with polyangitis (Churg–Strauss syndrome): a diagnostic rarity with an atypical presentation

Abstract

We report a case of a 33-year-old woman who presented to us with symptoms of bronchial asthma and peripheral neuropathy. After investigations, the diagnosis of eosinophilic granulomatosis and polyangitis (Churg-Strauss syndrome) was made.

References

  1. Jennette JC, Falk RJ, Bacon PA, Basu N, Cid MC, Ferrario F, et al. 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis Rheum 2013; 65:1–11.

    CAS  Article  Google Scholar 

  2. Comarmond C, Pagnoux C, Khellaf M, Cordier JF, Hamidou M, Viallard JF, et al. French Vasculitis Study Group Eosinophilic granulomatosis with polyangiitis (Churg–Strauss): clinical characteristics and long-term follow-up of the 383 patients enrolled in the French Vasculitis Study Group cohort. Arthritis Rheum 2013; 65:270–281.

    Article  Google Scholar 

  3. Langford C. Clinical features and diagnosis of small-vessel vasculitis. Cleve Clin J Med 2012; 79 Suppl 3:S3–S7.

  4. Lanham JG, Elkon KB, Pusey CD, Hughes GR. Systemic vasculitis with asthma and eosinophilia: a clinical approach to the Churg–Strauss syndrome. Medicine (Baltimore) 1984; 63:65–81.

    CAS  Article  Google Scholar 

  5. Jennette JC, Falk RJ, Andrassy K, Bacon PA, Churg J, Gross WL, et al. Nomenclature of systemic vasculitides. Proposal of an international consensus conference. Arthritis Rheum 1994; 37:187–192.

    CAS  PubMed  Google Scholar 

  6. Masi AT, Hunder GG, Lie JT, Michel BA, Bloch DA, Arend WP, et al. The American College of Rheumatology 1990 criteria for the classification of Churg–Strauss syndrome (allergic granulomatosis and angiitis). Arthritis Rheum 1990; 33:1094–1100.

    CAS  Article  Google Scholar 

  7. Kallenberg CG. Churg–Strauss syndrome: just one disease entity? Arthritis Rheum 2005; 52:2589–2593.

    Article  Google Scholar 

  8. Koldingsnes W, Nossent HC. Epidemiology of ANCA associated vasculitis. Norsk Epidemiologi 2008; 18:37–48.

    Google Scholar 

  9. Campos LE, Pereira LF. Pulmonary eosinophilia. J Bras Pneumol 2009; 35:561–573.

    Article  Google Scholar 

  10. Lhote F, Cohen P, Guilpain P, Guillevin L. Churg–Strauss syndrome. Rev Prat 2008; 58:1165–1174.

    PubMed  Google Scholar 

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Correspondence to Sujeet Raina.

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Raina, S., Kaul, R., Kaur, N. et al. Eosinophilic granulomatosis with polyangitis (Churg–Strauss syndrome): a diagnostic rarity with an atypical presentation. Egypt Rheumatol Rehabil 41, 187–189 (2014). https://doi.org/10.4103/1110-161X.147363

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  • DOI: https://doi.org/10.4103/1110-161X.147363

Keywords

  • antineutrophil cytoplasmic antibody
  • Churg-Strauss syndrome
  • revised nomenclature
  • systemic vasculitis