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Table 1 Clinical and laboratory characteristics of study patients (n = 30)

From: KL-6 in adult polymyositis and dermatomyositis patients and its correlation with interstitial lung disease

 

No

%

Muscle power

 Grade 0

1

3

 Grade 1

2

7

 Grade 2

2

7

 Grade 3

10

33

 Grade 3–4

5

17

 Grade 4

10

33

Dyspnea

 Free

15

50

 Mild

6

20

 Moderate

5

17

 Severe

4

13

Fatigue

 No

10

33

 Yes

20

67

Dry cough

 No

15

50

 Yes

15

50

Skin affection

 No

10

33

 Yes

20

67

 Mild

10

33

 Moderate

5

17

 Severe

5

17

Skin score

 Min.–Max

10.0–122.0

 

 Mean ± SD

85.48 ± 26.49

 

PFT

 FVC (L) Mean ± SD

1.81 ± 0.88

 

 FVC% Mean ± SD

54.0 ± 21.98

 

 FEV1 (L) Mean ± SD

1.83 ± 0.65

 

 FEV1% Mean ± SD

64.27 ± 18.24

 

CPk (U/L)

 Min.–Max

880–10,000

 

 Mean ± SD

7007.0 (1160–8500)

 

LDH (U/L)

 Min.–Max

350.0–1670.0

 

 Mean ± SD

931.84 ± 223.19

 

ALT (U/L)

 Min.–Max

45.0–343

 

 Median (IQR)

89.50 (60–167)

 

AST (U/L)

 Min.–Max

46.0–290

 

 Median (IQR)

88.50 (60–220)

 

KL-6 (U/ML)

 Min.–Max

75.0–1300

 

 Median (IQR)

744.50 (130.0–905.0)

 

Anti-Jo-1 (AU/ML)

 Negative

22 (73%)

 

 Positive

8 (27%)

 

ANA( IU/ML)

 Negative

10 (33)

 

 Positive

20 (67%)

 
  1. CDASI Cutaneous disease area and severity index, CPK Creatinine phosphokinase, LDH Lactate dehydrogenase, ALT Alanine transaminase, AST Aspartate aminotransferase, KL-6 Von den Lugen-6, ANA Antinuclear antibody, anti-Jo-1 Anti synthetase ab