Table 3 EUROFEVER/PRINTO classification criteria for FMF [11]

EUROFEVER/PRINTO clinical + genetic criteria > 6 criteria

Presence of confirmatory MEFV genotype and at least one among the following

1. Duration of episodes 1:3 days

2. Arthritis

3. Chest pain

4. Abdominal pain

OR

Presence of not confirmatory MEFV genotype and at least two among the following:

1. Duration of episodes 1:3 days

2. Arthritis

3. Chest pain

4. Abdominal pain

EUROFEVER/PRINTO clinical only criteria ≥ 6 criteria

Presence of:

1. Eastern Mediterranean ethnicity

2. Duration of episodes 13 days

3. Arthritis

4. Chest pain

5. Abdominal pain

Absence of:

1. Aphthous stomatitis

2. Urticarial rash

3. Maculopapular rash

4. Painful lymph nodes