| Mortality | P | |
---|---|---|---|
Survived (n = 737) | Died (n = 34) | ||
Personal history | |||
 Sex | |||
  Male | 59 (8%) | 4 (11.8%) | FEp = 0.351 |
  Female | 678 (92%) | 30 (88.2%) | |
 Age (years) | |||
  Mean ± SD. | 28.2 ± 8.7 | 28.4 ± 11.3 | 0.576 |
  Median (min.–max.) | 27 (12–60) | 27 (12–67) | |
 Age of onset | |||
  Mean ± SD. | 22.1 ± 8.6 | 23.1 ± 9.4 | 0.647 |
  Median (min.–max.) | 20 (2–52) | 20 (10–49) | |
 Duration (years) | |||
  Mean ± SD. | 6.1 ± 4.7 | 5.7 ± 5.4 | 0.223 |
  Median (min.–max.) | 5 (0.2–34) | 4 (0.3–22) | |
Lab | |||
 Anemia | 584 (79.2%) | 33 (97.1%) | 0.011* |
 Autoimmune | 136 (18.5%) | 9 (26.5%) | 0.242 |
 Leucopenia | |||
  Mean ± SD. | 0.6 ± 0.8 | 0.7 ± 0.8 | 0.264 |
  Median (min.–max.) | 0 (0–3.9) | 1 (0–3) | |
 Lymphopenia | 287 (38.9%) | 26 (76.5%) | < 0.001* |
 Neutropenia | 67 (9.1%) | 8 (23.5%) | FEp = 0.012* |
 Leucocytosis | 156 (21.2%) | 17 (50%) | < 0.001* |
 Thrombocytopenia | 151 (20.5%) | 18 (52.9%) | < 0.001* |
 Thrombocytosis | 102 (13.8%) | 9 (26.5%) | FEp = 0.075 |
Autoimmune profile | |||
 ANA | 696 (94.4%) | 31 (91.2%) | FEp = 0.435 |
 Anti-DNA | 483 (65.5%) | 19 (55.9%) | 0.248 |
 Decreased C3 | 434 (58.9%) | 29 (85.3%) | 0.002* |
 Decreased C4 | 359 (48.7%) | 22 (64.7%) | 0.068 |
 Anti Smith | 50 (6.8%) | 2 (5.9%) | FEp = 1.000 |